Abstract
Objective: To study, based on the literature, a case of Ebstein's Anomaly, exposing the clinical characteristics presented at the time and the patient's evolution, in the state of Espírito Santo. Case Details: Male, 62 years old, sought the specialized service complaining of fatigue and dyspnea. Past pathological history of hypertension, obesity, diabetes, heart failure, dextrocardia, cardiomegaly, Ebstein's anomaly, paroxysmal atrial fibrillation, and acute myocardial infarction. Family history of heart disease and drinking and smoking habits. On admission, he presented with progressive dyspnea NYHA IV functional classification. Transthoracic echocardiogram showed significant enlargement of the right chambers, grade I diastolic dysfunction and Ebstein's anomaly. He was operated on with tricuspid valve replacement (biological prosthesis No. 33) and coronary artery bypass graft surgery in the anterior descending, with cardiopulmonary bypass time of 142 minutes, without complications, progressing well and being discharged. Currently, the patient is at home, under follow-up. Final Considerations: Ebstein's anomaly is a congenital heart disease, usually managed and corrected in childhood, however, there are some individualized cases in adults. Its management must be differentiated, knowing its anatomical distinctions, hemodynamic variables, and associated morbidities, categorical for a good management of its carrier, reinvigorating their quality of life.