Keywords
Single umbilical artery
Esophageal atresia
Hypoplastic left heart syndrome
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Abstract
Objective: To report a dichorionic diamniotic twin pregnancy with intrauterine growth restriction (IUGR) in both fetuses, emphasizing the relationship between a two-vessel umbilical cord in one of the twins and its congenital anomalies, such as hypoplastic left heart syndrome (HLHS) and esophageal atresia. Case details: This is a dichorionic diamniotic pregnancy case in which one twin’s umbilical cord had only one artery (single umbilical artery, SUA) and its impacts, as this fetus presented with HLHS, among other conditions. Case report drawn from Texas Children’s Hospital and Materno Infantil Hospital from Goiânia/GO. Fetus 1 was born healthy, while Fetus 2 presented multiple anomalies, including HLHS, esophageal atresia and a single umbilical artery. If left untreated, HLHS leads to high mortality within the first months of life, whereas esophageal atresia may cause serious complications, such as asphyxia and pneumonia. Final considerations: Early diagnosis, by fetal echocardiography and Doppler, proved to be crucial for appropriate management and better neonatal outcomes, as well as the multidisciplinary approach in handling the case.
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