Keywords
Primary amenorrhea
Rudimentary uterus
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Abstract
Objective: Presenting a case of a patient with Müllerian malformation and cervix agenesis, which results from an anomalous fusion of the müllerian ducts during embryogenesis. Case detailing: Female, 19 years old, complaining of primary amenorrhea and ciclic pelvic pain for 4 years. At physical examination was noticed that the patient had normal secondary sexual characters and a short blind-folded vagina. Complimentary exams showed two uterine cavities which were completely divided, but with no endocervical canal in both cavities. Furthermore, the endometrium was functioning. The terapeutic plan, besides the psychological following, was perform a hysterectomy accompanied by a salpingectomy followed by treatment with vaginal dilators. Final considerations: It's imprescindible that physicians know how to procede when in presence of a patient with a müllerian malformation. It must be evidenced the importance of an individual avaliation to choose the best therapeutic option, as there are a variable range of how these malformations present themselves.
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