Care for children with cystic fibrosis

Abstract

Objective: To summarize scientific production on the care of children with cystic fibrosis. Methods: This is an integrative review, with a search carried out between June and September 2023 in the databases: Pubmed, BDENF, LILACS and SCOPUS in the period between 2010 and 2023. Results: The sample consisted of 10 studies available in the databases Pubmed and SCOPUS data. The selected studies addressed general care which can be considered within the spectrum of nursing practice, only one study focused on nursing, although it did not use any supporting theory. The care identified focused on aspects of care management, guidance on nutrition, physical activity, frequency of assessments, exams to be performed, drug and non-drug therapies, identification of signs and symptoms of clinical deterioration, pain management, management strategies, adherence to treatment, educational interventions, in addition to interventions related to psychological and emotional impacts and coping. Final considerations: There is a gap in the literature on how nursing has assisted this clientele and organized its work, and this gap is even greater in the Brazilian context. The lack of specialized professionals, high turnover, lack of standardization of care and instruments that guide clinical practice, especially for nursing professionals, are still bottlenecks that need to be overcome.