Abstract
Objective: To describe a rare case of bile duct cyst and to analyze the complex surgical approach to the cyst, showing the possibility of a good prognosis and quality of life for patients with choledochal cyst. Case Report: Fourteen-year-old patient, female, with no previous comorbidities, with jaundice, abdominal pain, and exhibiting hyporexia and alcholic stools. Imaging examination identified a cystic mass located at the head of the pancreas. Patient was sent to the general surgery unit at Santa Casa de Misericórdia of Belo Horizonte (SCMBH), and imaging and laboratorial examination confirmed the diagnosis. Upon clinical worsening, patient underwent gastroduodenopancreatectomy and cholecystectomy with reconstruction in two separate loops in Roux-en-Y. Final Considerations: The most recent Todani and Alonso Lej classification divides cysts into six different types, varying by their topography and cyst presentation. It’s extremely important to make an early diagnosis and take the right actions in time, in order to avoid severe complications.