Abstract
Objective: To report the coexistence between Adult-Onset Still's Disease and Pulmonary Arterial Hypertension. Details of the case: We present the case of a 29-year-old pregnant woman, referred by the rheumatology service of a hospital in the state of São Paulo with a diagnosis of Adult-Onset Still’s Disease. She had persistent fever, arthralgia, bilateral wrist arthritis, pericarditis, pleural effusion, elevated ferritin, lymphadenopathy and visceromegaly at the onset of the disease. A cesarean delivery was performed and, two months later, he used progressive doses of prednisolone, after relapse of the disease. She had an evolution of the condition with the same symptoms, but associated with pulmonary hypertension on echocardiographic examination. Transferred to the University of São Paulo for cardiac catheterization. During the examination, she had cardiorespiratory arrest, with no response to resuscitation maneuvers. Final considerations: Adult Still's Disease is a rare condition characterized by fever, arthralgia and maculopapular rash that is difficult to walk with Pulmonary Arterial Hypertension. Thus, greater knowledge about the disease is needed by the medical community, in order to prevent its progression and complications.