Keywords
Polymyositis
Rare deseases
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Abstract
Objective: The present study aimed to describe the simultaneous association of two connective tissue diseases, of an autoimmune nature, being composed of systemic sclerosis (ES) and polymyositis (PM). Demonstrating the rarity of the overlap and the importance of including it as a diagnostic hypothesis for these rheumatological patients. Details of the case: Male patient, 39 years old, with previous diagnosis of idiopathic pulmonary fibrosis, with dyspnea on exertion, Raynaud's phenomenon, arthralgia and proximal muscle weakness. The presence of positive rheumatological markers and muscle enzymes was found. As standard antinuclear factor (ANA) 1/320: dotted and nucleolar nuclear type mixed, ANTI-SCL 70 ≥ 240 and elevation in aldolase / creatine phosphokinase. Final considerations: The need for further epidemiological studies and the performance of specific protocols for a better diagnostic and therapeutic approach for these types of cases, since the relationship between systemic sclerosis and polymyositis represents one of the most unusual overlapping syndromes in the literature.