Abstract
Objective: To report the clinical case of a patient with arrhythmogenic right ventricular cardiomyopathy / dysplasia, from the beginning of the clinical presentation until the diagnosis was established, followed up at a cardiology hospital in a city in the state of Amazonas. Case details: Patient, after starting palpitation, dyspnea and chest pain, sought an emergency care unit where monomorphic ventricular tachycardia was found and chemical cardioversion with amiodarone was initiated, but evolved to ventricular fibrillation and cardiorespiratory arrest with return of spontaneous circulation after cardiopulmonary resuscitation maneuvers and electrical defibrillation. Subsequently, he was submitted to complementary exams and these added to the clinical history and physical exam allowed the diagnosis of the patient as having arrhythmogenic right ventricular cardiomyopathy/dysplasia; as a treatment, he underwent a cardioverter-defibrillator implant and was medicated with sotalol and losartam. Final considerations: The follow-up of this case shows one of the forms of initial manifestation of the disease, its diagnostic difficulty and yet the possibility of being performed without the use of invasive exams.